2025, Vol. 8, Issue 1, Part A

Author(s)
Mariam Iddi Kaoneka, Erick Michael Mbuguje, Lilian Evaristo Salingwa and Debora Hoza

Abstract
Renal angiomyolipoma is a rare, typically benign tumor with distinct radiological features and is often associated with Tuberous Sclerosis Complex. These tumors can develop both micro- and macro-aneurysms, which have the potential to rupture, leading to retroperitoneal bleeding. We herein present the case of a 39-year-old female with Tuberous Sclerosis Complex who presented with acute right-sided flank pain, bilateral tender flank masses, chest pain, a productive cough, and facial angiofibromas. Abdominal CT revealed retroperitoneal hemorrhage on the right side, along with bilateral angiomyolipomas. High-resolution CT of the chest showed features of lymphangioleiomyomatosis, while a brain CT revealed subependymal hamartomas of varying sizes. Multiple microaneurysms (<4 cm) were identified in both kidneys, with a single macroaneurysm (>4 cm) in the right kidney being the source of the retroperitoneal bleeding. The patient underwent transarterial embolization using Polyvinyl Alcohol particles and embolization coils. This case underscores the importance of considering prophylactic embolization in patients with giant angiomyolipomas and aneurysms larger than 4 cm to prevent potential rupture and its associated complications.

DOI: https://doi.org/10.33545/26644436.2025.v8.i1a.435

Pages: 45-49 | Views: 165 | Downloads: 64